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AMACR Recombinant Rabbit mAb

簡(jiǎn)要描述:This gene encodes a racemase. The encoded enzyme interconverts pristanoyl-CoA and C27-bile acylCoAs between their (R)- and (S)-stereoisomers. The conversion to the (S)-stereoisomers is necessary for degradation of these substrates by peroxisomal beta-oxidation. Encoded proteins from this locus localize to both mitochondria and peroxisomes. Mutations in this gene may be associated with adult-onset sensorimotor neuropathy, pigmentary retinopathy, and adrenomyeloneuropathy due to defects in bi

  • 產(chǎn)品型號(hào):bsm-60430R
  • 廠商性質(zhì):生產(chǎn)廠家
  • 更新時(shí)間:2025-02-26
  • 訪  問(wèn)  量: 113

詳細(xì)介紹

Human
WB,IHC-P,IHC-F,IF
Shipped at 4℃. Store at -20℃ for one year. Avoid repeated freeze/thaw cycles.

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